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Review Article| Volume 102, ISSUE 5, P873-882, October 2022

Meconium Ileus, Distal Intestinal Obstruction Syndrome, and Other Gastrointestinal Pathology in the Cystic Fibrosis Patient

Published:September 07, 2022DOI:https://doi.org/10.1016/j.suc.2022.07.016

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      References

        • Kleven D.T.
        • McCudden C.R.
        • Willis M.S.
        Cystic fibrosis: newborn screening in America.
        MLO Med Lab Obs. 2008; 40 (22, 4-18): 16-18
        • Sathe M.
        • Houwen R.
        Meconium ileus in cystic fibrosis.
        J Cyst Fibros. 2017; 16: S32-S39
        • Colombo C.
        • Ellemunter H.
        • Houwen R.
        • et al.
        Guidelines for the diagnosis and management of distal intestinal obstruction syndrome in cystic fibrosis patients.
        J Cyst Fibros. 2011; 10: S24-S28
        • Escobar M.A.
        • Grosfeld J.L.
        • Burdick J.J.
        • et al.
        Surgical considerations in cystic fibrosis: a 32-year evaluation of outcomes.
        Surgery. 2005; 138 ([discussion: 71-2]): 560-571
        • DeLorimier A.A.
        • Fonkalsrud E.W.
        • Hays D.M.
        Congenital atresia and stenosis of the jejunum and ileum.
        Surgery. 1969; 65: 819-827
        • Dicke J.M.
        • Crane J.P.
        Sonographically detected hyperechoic fetal bowel: significance and implications for pregnancy management.
        Obstet Gynecol. 1992; 80: 778-782
        • Lince D.M.
        • Pretorius D.H.
        • Manco-Johnson M.L.
        • et al.
        The clinical significance of increased echogenicity in the fetal abdomen.
        AJR Am J Roentgenol. 1985; 145: 683-686
        • Opinion No Committee
        691: Carrier screening for genetic conditions.
        Obstet Gynecol. 2017; 129: e41-e55
        • Ziegler M.M.
        Meconium ileus.
        Curr Probl Surg. 1994; 31: 731-777
        • Farrell P.M.
        • White T.B.
        • Ren C.L.
        • et al.
        Diagnosis of cystic fibrosis: consensus guidelines from the cystic fibrosis foundation.
        J Pediatr. 2017; 181s: S4-S15.e1
        • Rowe M.I.
        • Furst A.J.
        • Altman D.H.
        • et al.
        The neonatal response to gastrografin enema.
        Pediatrics. 1971; 48: 29-35
        • Carlyle B.E.
        • Borowitz D.S.
        • Glick P.L.
        A review of pathophysiology and management of fetuses and neonates with meconium ileus for the pediatric surgeon.
        J Pediatr Surg. 2012; 47: 772-781
        • Jaffe B.F.
        • Graham 3rd, W.P.
        • Goldman L.
        Postinfancy intestinal obstruction in children with cystic fibrosis.
        Arch Surg. 1966; 92: 337-343
        • Hort A.
        • Hameed A.
        • Middleton P.G.
        • et al.
        Distal intestinal obstruction syndrome: an important differential diagnosis for abdominal pain in patients with cystic fibrosis.
        ANZ J Surg. 2020; 90: 681-686
        • Houwen R.H.
        • van der Doef H.P.
        • Sermet I.
        • et al.
        Defining DIOS and constipation in cystic fibrosis with a multicentre study on the incidence, characteristics, and treatment of DIOS.
        J Pediatr Gastroenterol Nutr. 2010; 50: 38-42
        • Littlewood J.M.
        Cystic fibrosis: gastrointestinal complications.
        Br Med Bull. 1992; 48: 847-859
        • Zahra M.
        • Frederick C.
        • Thomas R.
        • et al.
        Gastrografin enemas for treatment of distal intestinal obstruction syndrome in children and adults with cystic fibrosis.
        J Pharm Nutr Sci. 2014; 4: 76-80
        • Shidrawi R.G.
        • Murugan N.
        • Westaby D.
        • et al.
        Emergency colonoscopy for distal intestinal obstruction syndrome in cystic fibrosis patients.
        Gut. 2002; 51: 285-286
        • Nousia-Arvanitakis S.
        Cystic fibrosis and the pancreas: recent scientific advances.
        J Clin Gastroenterol. 1999; 29: 138-142
        • Durie P.R.
        • Forstner G.G.
        Pathophysiology of the exocrine pancreas in cystic fibrosis.
        J R Soc Med. 1989; 82: 2-10
        • Stefano M.A.
        • Poderoso R.E.
        • Mainz J.G.
        • et al.
        Prevalence of constipation in cystic fibrosis patients: a systematic review of observational studies.
        J Pediatr (Rio J. 2020; 96: 686-692
        • El-Chammas K.I.
        • Rumman N.
        • Goh V.L.
        • et al.
        Rectal prolapse and cystic fibrosis.
        J Pediatr Gastroenterol Nutr. 2015; 60: 110-112
        • Waldhausen J.H.T.
        • Richards M.
        Meconium ileus.
        Clin Colon Rectal Surg. 2018; 31: 121-126
        • Coughlin J.P.
        • Gauderer M.W.
        • Stern R.C.
        • et al.
        The spectrum of appendiceal disease in cystic fibrosis.
        J Pediatr Surg. 1990; 25: 835-839